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CHROMOSOME 22Q11.2 DELETION SYNDROME

 
  CHARGE Syndrome

 

Patients have coloboma of the iris or retina and simple malformed ears (small ears, cup-shaped, lop ears).  Facial nerve palsy may lead to facial asymmetry.  Micrognathia and microcephaly may also be present.  Patients may have a spectrum of T-cell immune deficiency that may range from mild T-cell lymphopenia to an almost complete absence of T-cells resulting in a severe combined immune deficiency phenotype.

CHARGE Syndrome

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